... Canada.31University of Auckland, Auckland, NewZealand.32Department of Internal Medicine, University of Cincinnati,Cincinnati, Ohio, USA.33Department of Clinical and Experimental Medicine,County Hospital ... outandC1-INHfunctionalassayshouldbeobtained(inalaboratory skilled in functional C1-INH assay with care-ful sample drawing, handling, shipping, and interpretingresults) [8,18,19,28,29,34]. If C1-INH functional activityis low with ... randomized clinical trials with plasma-derived C1 inhibitor replacement therapy(pdC1INH;[1,2]) and a few clinical trials using andro-gens and antifibrinolytics [3-5]. C1-esterase inhibitorconcentrates...