... stress;very long chain acyl-CoA dehydrogenase(VLCAD) de ciencyCorrespondenceS. Tucci, Department of General Pediatrics,University Children’s Hospital,Moorenstraße 5, D-40225 Duesseldorf,GermanyFax: ... commonb-oxidation defect of long-chain fatty acids, with anincidence of one in 55 000 to one in 100 000 births [1].VLCAD de ciency (VLCADD) presents heterogeneousclinical phenotypes, with different severities ... Strauss (currently Cincinnati Children’sHospital, OH, USA), and were generated as describedin detail previously [36]. Experiments were performed onfourth-generation to fifth-generation intercrosses...