... Management of SickleCellDiseaseinChildren Page 14 of 15 Appendix Monitoring Guidelines for Patients Receiving Intravenous Opioid Analgesia: Analgesia Continuous Opioid Infusion Intermittent ... 15-20% of infants and young children with sicklecell anemia die before the age of 5, usually of septicemia or meningitis Inchildren under years of age with sicklecell disease, the predominant ... in a SickleCell Clinic Guidelines for Specific Clinical Settings: A Acute Painful Episode (Vaso Occlusive Disease) A vaso-occlusive crisis (VOC) is the most frequent complication of Sickle Cell...
... overwhelming majority of parents having children with sicklecelldiseasein Africa live and die without tests needed to establish the correct diagnosis Most infants with sicklecelldisease are ... prevention of sicklecelldisease and attitude towards their children with sicklecelldisease Table 4: Participants’ knowledge about causes of sicklecelldisease and attitudes towards children Variable ... causes of sicklecelldisease and their attitudes toward children with sicklecelldisease Table 2: Relationship of sex and attitude of the participants toward children with sicklecelldisease Variable...
... syndrome insicklecell haemoglobinopathy J Bone and Joint Surg (Br) 1995, 77B:310-312 11 Acurio MT, Friedman RJ: Hip Arthroplasty in patients with sicklecell Haemoglobinopathy J Bone and Joint Surg ... Homozygote sicklecelldiseasein patients above 20 years of age: follow-up of patients in Dakar Rev Med Interne 2003, 24:711-715 25 Platt OS, Brambilla DJ, Rosse WF: Mortality insicklecell disease, ... Surgery 1992, 2:145-148 19 Lindberg L, Lindgren L: Bone and Joint infections Int Orthop 1997, 1:191198 20 Nade S: Acute septic arthritis in infancy and children J Bone and Joint Surg 1983, 65B:234-241...
... vital signs and maintaining them within tight ranges Anaesthesia from the beginning up to the end of surgery lasted 80 minutes Postoperative care, including fluid management and weaning off the respirator ... USA for his assistance in editing this manuscript Authors’ contributions RJ was involved in conceiving, designing and writing this manuscript MT was involved in providing a description of the ... Anesthesiological management in patients with sicklecelldisease Anesthesiol Intensivmed Notfallmed Schmerzther 2002, 37:104-108 14 Oginni LM, Rufai HB: How safe is tourniquet use insicklecell disease? Afr...
... A., & Zemel, B S (2004) Low vitamin D status inchildren with sicklecelldisease Journal of Pediatrics, 145, 622-627 Center for Disease Control (2010) SickleCell Disease: Data and Statistics Retrieved ... study examining vitamin A status inchildren with SCD-SS revealed that the mean serum retinol level was suboptimal in 66% of the children (Schall, Zemel, Kawchak, Ohene-Frempong, & Stallings, 2004) ... studies examining vitamin D, vitamin A, and zinc status suggest that increased nutritional demands are likely contributing factors to the micronutrient deficiencies seen in SCD-SS Affected children...
... in determining discriminant validity of the PedsQL™ Family Impact Module in our population of children with sicklecell disease, we collected data on the disease status of the children with sickle ... of children with severe sicklecelldisease reported significantly worse scores in the communication and worry scales than children with mild sicklecelldisease and children without sicklecell ... children with and without sicklecelldiseaseIn addition, we also compared parents of children with sicklecelldisease to parents of children without sicklecelldisease and without other co-morbidities...
... life inchildren with sicklecelldisease J Behav Med 2002, 25:269-283 15 Palermo TM, Riley CA, Mitchell BA: Daily functioning and quality of life inchildren with sicklecelldisease pain: relationship ... functioning of children with sicklecelldisease and comparison peers Journal of Pediatric Hematology/Oncology 2004, 26:642-648 11 Panepinto JA: Health-related quality of life insicklecelldisease ... of HRQoL, encompassing all three components of children s well-being, is still in its infancy inchildren with SCD [11] For example, compared to over 400 studies on HRQoL inchildren with cancer,...
... of research investigating patients with concomitant asthma and sicklecelldisease Table 2: Results inchildren with sicklecelldisease with and without asthma Patients with SickleCell & Asthma ... pulmonary failure Medicine 1998, 67:66-76 Nickerson B, Browning I, Vichinsky E, Weiner S: Cooperative Study of SickleCellDisease Pulmonary function inchildren with sicklecelldisease (abstract) ... compared to children with sicklecelldisease alone The significance of these findings relates to the hypothesis that appropriately aggressive treatment of asthma inchildren with sicklecell disease...
... GVHD is initiated, T-cells produce additional proinflammatory cytokines, including tumor necrosis fac tor (TNF)-α, interferon (IFN)-γ, and interleukin (IL)-2, which in turn attract more T-cells ... (Th2) cells can initiate a response against autoantigens leading to B -cell hyperre activity and production of autoantibodies, causing targetorgan damage, including skin, mucosa, eyes, joints, ... rash and itching may occur; the skin may become scaly; the skin may heal by scarring; hair loss may accompany the skin injury Look for dry eyes: no tears, constant rubbing and blinking; sensitivity...
... major genotypes within the definition of SCD: homozygous sicklecell (SS) disease, sickle haemoglobin C (SC) disease, sicklecell bz thalassaemia (S bz thalassaemia) and sicklecell b0 thalassaemia ... endocrine cause.3 Determination of gonadotropin concentrations in 40 children with sicklecell anaemia (5–16 yrs) showed a significant increase in LH inchildren aged 5–10 years and normal levels in ... composition inchildren with sicklecelldisease Am J Clin Nutr 2002; 76:218–25 63 Badaloo A, Jackson AA, Jahoor F Whole body protein turnover and resting metabolic rate in homozygous sicklecell disease...
... treatment seeking for pain from sicklecell disease: qualitative study British Medical Journal, 318, 1585–1590 McCrae, J.D & Lumley, M A (1998) Health status insicklecell disease: examining the roles ... Keith, B.R., Tota-Faucette, M., Noll, S & Kinney, T.R (1993) Sicklecelldisease pain inchildren and adolescents: change in pain frequency and coping strategies over time Journal of Pediatric ... stress insicklecell disease: an analysis of daily pain records International Journal of Behavioural Medicine, 5, 185–203 Powars, D.R (2000) Management of cerebral vasculopathy inchildren with sickle...
... Guidelines for the management of the acute painful crisis insicklecelldisease Br J Haematol 2003, 120(5):744-752 Serjeant GR: The dilemma of defining clinical severity in homozygous sicklecell ... death in patients with sicklecelldisease Blood 2006, 107(6):2279-2285 Steinberg MH: Predicting clinical severity insicklecell anaemia Br J Haematol 2005, 129(4):465-481 Cumming V, King L, ... DH: Sicklecell disease: Pain, coping and quality of life in a study of adults in the UK Br J Health Psychol 2002, 7(Part 3):331-344 Anie KA, Steptoe A: Pain, mood and opioid medication use in sickle...
... Guidelines for the management of the acute painful crisis insicklecelldisease Br J Haematol 2003, 120(5):744-752 Serjeant GR: The dilemma of defining clinical severity in homozygous sicklecell ... death in patients with sicklecelldisease Blood 2006, 107(6):2279-2285 Steinberg MH: Predicting clinical severity insicklecell anaemia Br J Haematol 2005, 129(4):465-481 Cumming V, King L, ... DH: Sicklecell disease: Pain, coping and quality of life in a study of adults in the UK Br J Health Psychol 2002, 7(Part 3):331-344 Anie KA, Steptoe A: Pain, mood and opioid medication use in sickle...
... depression and loneliness in this disease group Methods Sampling The Jamaica SickleCell Cohort Study (JSCCS) incorporates all patients with SCD detected during the screening of 100,000 consecutive ... comprehensive sicklecell clinic (SCU) located at the University of the West Indies in Kingston, Jamaica for routine health maintenance checks and for all significant sick events in an effort ... frequent painful crises and lower prevalence of leg ulceration (results not shown) This finding may point to lower coping mechanisms in those with the less severe form of disease; past findings have...
... index of clinical severity in individuals with sicklecell anemia Am J Hematol 1992, 41:227-231 58 Natta C, Machlin L, Brin M: A decrease in irreversibly sickle erythrocytes insicklecell anemia ... capacity in paediatric patients with homozygous sicklecelldisease Eur J Clin Nutr 1989, 43:609-614 63 Houston PE, Rana S, Sekhsaria S, Perlin E, Kim KS, Castro OL: Homocysteine insicklecell disease: ... endothelial cells to RBCs sickled in vitro results in a fourfold to eightfold induction of endothelin-1 mRNA [51] Similarly, we demonstrated increased endothelin-1 mRNA and protein levels in endothelial...
... infarction in a thirty five year old patient with Sicklecell Hemoglobin C disease (Hb SC) That psychosis in this patient was complicating brain tissue silent infarcts cannot be ruled out in view ... children with sicklecelldisease Dev Med Child Neurol 1991, 33(12):1087-94 Yang YM, Cepeda M, Price C, Shah A, Mankad V: Depression inchildren and adolescents with sicklecelldisease Arch Pediatr ... Psychiatric morbidity in patients with sicklecell anemia West Afr J Med 1996, 15(4):196-200 Pegelow CH, Wang W, Granger S, Hsu LL, et al.: Silent infarcts inchildren with sicklecell anemia and abnormal...
... Occasional abdominal pain, difficulty gaining weight and height Prior history of anemia Difficulty gaining weight and height Prior history of anemia Frequent abdominal pain, difficulty gaining weight ... covering socioeconomic and demographic aspects as well as complaints related to celiac disease (abnormal intestinal rhythm, abdominal pains, flatulence, recurrent aphthous ulcers, difficulty gaining ... gastroenterology clinic to continue investigation of celiac disease Data were stored in Epi-Info version 6.0 Seropositivity was calculated as the proportion of individuals in the sample with...
... invasive examination method, we fundamental when dealing with chronic patients indicated lung biopsy, since it offers more objective informa- Epidemiological research into interstitial lung diseases ... Clinical presentation of interstitial lung diseaseinchildren Pediatr Respir Rev 2004;5:98-100 19 Barbato A, Panizzolo C, Cracco A, de Blic J, Dinwiddie R, Zach M Interstitial lung diseasein ... patients Wheezing is less common but of ILD inchildren and, in our hospital, became available only it was observed in 11 patients in 1997 As a result, in five cases HRCT scans were not In the 13...
... Laboratories, Washington DC, 1999 SickleCellDisease Guideline Panel SickleCell Disease: Screening, Diagnosis, Management, and Counseling in Newborns and Infants Clinical Practice Guideline No AHCRP ... Gallagher D, Kinney TR, et al Mortality inchildren and adolescents with sicklecelldisease Pediatrics 1989;84:500-8 SickleCellDisease Guideline Panel SickleCell Disease: Screening, Diagnosis, ... Genet 1991;48:452-9 SickleCellDisease Guideline Panel SickleCell Disease: Screening, Diagnosis, Management and Counseling in Newborns and Infants Clinical Practice Guideline No AHCPR Pub No...