... to respiratory, pancreatic, and gastrointestinal disorders [1] Forty years ago, CF was invariably a fatal disease of early childhood Although the disease remains incurable, advances in CF chronic ... education and training of health careers explains that its daily practice was generalized in ICU only since 1999 [9] Impact of NIV implementation has been poorly evaluated for CF patients hospitalized ... ns Acute episode characteristics SAPSII PaO2 at entry, mmHg PaCO2 at entry, mmHg Arterial pH at entry Admission for pulmonary exacerbation Length of NIV, days Length of ICU stay, days ICU mortality, ...