... synthase gene; Gb4, globotetraosylceramide (GalNAcb1,3Gala1,4LacCer); GD 1a, NeuAca2,3Galb1,3GalNAcb1,4(NeuAca2,3)LacCer; GD1b, Galb1,3GalNAcb1,4(NeuAca2,8NeuAca2,3)LacCer; GM1, Galb1,3GalNAcb1,4(NeuAca2,3)LacCer; ... Fan JQ, Ishii S, Asano N & Suzuki Y (1999) Acceler-ated transport and maturation of lysosomalalpha-galactosidase A in Fabry lymphoblasts by anenzyme inhibitor. Nat Med 5, 112–115.29 Mattocks ... relative luciferaseactivity as a percentage of the luciferaseactivity of untreated cells. Error bars,mean ± SD, n = 2. (B) Time -dependent alteration of luciferase activity of HML-Gb3cells after...